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Case
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Diagnosis
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Macroscopic analysis (atrophy pattern)
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Microscopic analysis
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1
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rtvFTD
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Frontotemporal predominant R-FT > L-FT
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FTLD-TDP type B + MND
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2
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rtvFTD
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Frontotemporal predominant R-FT = L-FT
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FTLD-TDP type E
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3
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rtvFTD
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Frontotemporal predominant R-FT > L-FT
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FTLD-tau-MAPT
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4
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rtvFTD
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Frontotemporal predominant R-FT = L-FT
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FTLD-FUS
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5
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rtvFTD
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Temporal predominant R-T = L–T
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FTLD-TDP type C
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- rtvFTD: right temporal variant frontotemporal dementia; svPPA: semantic variant primary progressive aphasia; R: right; L: left; F: frontal; T: temporal; TDP: TAR DNA-binding protein 43; TAU: tau protein; MND: motor neuron disease; MAPT: microtubule associated protein; FUS: fused in sarcoma protein; PiD: Pick’s disease